Lies nach, dann ist es vielleicht nicht so lustig für die Leute, die es haben.
Living with PKU requires a limited diet and very careful management. If left unmanaged, PKU can lead to devastating consequences, such as brain damage. People living with PKU do not have the ability to metabolize the amino acid phenylalanine (Phe) found in many foods and they require supplementation of amino acid-based foods for special medical purposes (FSMPs) to prevent protein deficiency and optimize metabolic control. Currently available FSMPs lead to poor or suboptimal clinical outcomes and compliance because they are rapidly absorbed and are characterized by an unpleasant odor and aftertaste. Such factors contribute to barriers to social interaction for PKU patients, further limiting FSMP compliance and exposing patients to the risks of poor disease control.
ABOUT PKU GOLIKE®
PKU GOLIKE® products are phenylalanine-free foods for special medical purposes (FSMPs) for both children and adults. The PKU GOLIKE line of products are comprised of a mixture of amino acids in the form of granules and available in convenient packets (PKU GOLIKE Plus® 3-16 and 16+), medical food bars (PKU GOLIKE BAR®) and tablets to be chewed (PKU GOLIKE KRUNCH®). Developed with the company's proprietary, patent-protected Physiomimic Technology™ platform, PKU GOLIKE products are the first prolonged-release amino acid FSMPs, characterized by a special coating that ensures physiological absorption of the amino acids mirroring that of natural proteins. The special coating also masks the unpleasant taste, odor and aftertaste of the amino acids. PKU GOLIKE granules are flavorless and can be mixed with many of your favorite foods. PKU GOLIKE products contain all 19 amino acids that people with PKU need to maintain neurological and muscular health and is fortified with 27 essential vitamins and minerals, including ones normally found in protein-rich foods like iron, calcium and vitamin B12. PKU GOLIKE products have been commercially available in Europe since 2018 and in the U.S. since October 2022. For more information in Europe, please visit: https://www.apr.ch/apr-pharma-products/medical-prescription/pku-golike-family/. You can also follow our Twitter and Facebook pages.
ABOUT PHENYLKETONURIA (PKU)
Phenylketonuria (PKU) is a rare inherited disorder affecting more than 450,000 patients worldwide. PKU is caused by a defect of the enzyme needed to break down phenylalanine (Phe), leading to a toxic buildup of Phe from the consumption of foods containing protein or aspartame. Untreated PKU can result in global developmental delay or severe irreversible intellectual disability, as well as growth failure, hypopigmentation, motor deficits, ataxia and seizures. Treatment of PKU is lifelong to avoid these serious consequences and people living with PKU must follow a strict diet that limits intake of Phe from infancy onward. People living with PKU require supplementation of amino acids formulated as foods for special medical purposes (FSMP) to prevent protein deficiency.
sorry, falsch ausgedrückt.....Ich fand den Preis eines "Riegels" sehr hoch. Für mich ist ein Riegel etwas zum Essen (bei Sport oder als Nahrungsergänzung usw.). Ich wollte damit nicht die Krankheit verharmlosen oder mich über die betroffenen Patienten lustig machen....